CDE Detailed Report
Disease: Friedreich's Ataxia
Sub-Domain: Ataxia and Performance Measures
CRF: Friedreich's Ataxia Rating Scale (FARS)
Displaying 51 - 90 of 90
Sub-Domain: Ataxia and Performance Measures
CRF: Friedreich's Ataxia Rating Scale (FARS)
Displaying 51 - 90 of 90
| CDE ID | CDE Name | Variable Name | Definition | Short Description | Question Text | Permissible Values | Description | Data Type | Disease Specific Instructions | Disease Specific Reference | Population | Classification (e.g., Core) | Version Number | Version Date | CRF Name (CRF Module / Guideline) | Sub Domain Name | Domain Name | Size | Input Restrictions | Min Value | Max Value | Measurement Type | External Id Loinc | External Id Snomed | External Id caDSR | External Id CDISC |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| C11804 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam gait duration | FARSNeuroExmUprtStabltyGaitDur | Time in seconds for completion of the gait test in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Time in seconds for completion of the gait test in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Time in seconds | Numeric Values |
Use stopwatch. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Free-Form Entry |
second | |||||||||
| C11740 | Friedreich's Ataxia Rating Scale (FARS) - daily activities swallowing score | FARSDailyActivsSwallowScore | Swallowing score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS) | Swallowing score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS | Swallowing | 0;0.5;1;1.5;2;2.5;3;3.5;4 | 0 - Normal;;1 - Rare choking (< once a month);;2 - Frequent choking (< once a week, > once a month);;3 - Requires modified food, chokes multiple times a week, or patient avoids certain foods;;4 - Requires NG tube or gastrostomy feedings | Numeric Values |
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11772 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral nerve system muscle atrophy right score | FARSPNSNeuExMuscAtrphRtScore | Score for right-side muscle atrophy in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for right-side muscle atrophy in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Muscle Atrophy | 0;1;2 | 0 - None;1 - Present - mild/moderate;2 - Severe/total wasting | Numeric Values |
Score most severe atrophy in either upper or lower limb. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11815 | Friedreich's Ataxia Rating Scale (FARS) - instrumental testing 9 hole peg test left trial 2 duration | FARSInstrTest9HPTLftTry2Dur | Duration in seconds for participant/subject to complete left-hand trial 2 of the 9-hole peg test in the instrumental testing section, as part of the Friedreich's Ataxia Rating Scale (FARS) | Duration in seconds for participant/subject to complete left-hand trial 2 of the 9-hole peg test in the instrumental testing section, as part of the Friedreich's Ataxia Rating Scale (FARS | Trial 2 | Numeric Values |
Make sure the stopwatch is set to zero. Start timing as soon as the patient touches the first peg, and stop timing when the last peg hits the container. The total time to complete the task is recorded in seconds including one decimal place, rounded as needed. Round up to the next tenth if hundredths place is > = .05, round down if hundredths place is |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Free-Form Entry |
second | |||||||||
| C11751 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam bulbar cough score | FARSNeuroBulbrCoughScore | The score for forcefulness of cough in the bulbar portion of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | The score for forcefulness of cough in the bulbar portion of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Cough | 0;0.5;1;1.5;2 | 0 - Normal;;1 - Depressed;;2 - Totally or nearly absent | Numeric Values |
Rate each item on the basis of the patient status during examination. To the extent possible, sequential patient examinations should be carried out at the same time of the day. If the patient is taking any medication, the examination should be carried out prior to dosing, or at a fixed time following the dosing based on the maximum expected therapeutic response. Increments of 0.5 may be used if examiner feels an item falls between 2 defined severities. Patient asked to cough forcefully 3 times. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11783 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability footwear indicator | FARSNeurExUprtStabltyFootwrInd | Indicator whether participant/subject is barefoot or wearing footwear for standing and walking assessments for Part 3: Neurological Examination E. Upright Stability, as part of the Friedreich's Ataxia Rating Scale (FARS) | Indicator whether participant/subject is barefoot or wearing footwear for standing and walking assessments for Part 3: Neurological Examination E. Upright Stability, as part of the Friedreich's Ataxia Rating Scale (FARS | BarefootFootwear | Barefoot;Footwear | Barefoot;Footwear | Alphanumeric |
For standing and walking assessment instruct patient to wear best walking shoes and record below if barefoot, footwear used. Stance and gait tests may be done barefoot if patient does not have appropriate footwear, however, it should be done the same way for serial measurement. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11794 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability tandem stance trial 1 duration | FARSNEUpStTanStanceTr1Dur | Duration in seconds of tandem stance trial 1 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Duration in seconds of tandem stance trial 1 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Trial 1 | 0;1;2;3;4 | 0 - 1 minute or longer;1 - <1 minute, >45 sec;2 - <45 sec, >30 sec;3 - <30 sec, >15 sec;4 - <15 sec or needs hands held by assistant/device | Numeric Values |
For tandem stance, the dominant foot is in the back and the heel of the other foot is lined with the toes of the dominant foot but not in front of the toes (because this makes it even more difficult). Stance and gait tests may be done barefoot if patient does not have appropriate footwear, however, it should be done the same way for serial measurement. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
second | |||||||
| C17533 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral nerve system vibratory sense toe left duration | FARSPNSNeuExVibSenToeLtDur | Delay in seconds before participant/subject feels vibration in the left-side toes, as part of the Friedreich's Ataxia Rating Scale (FARS) | Delay in seconds before participant/subject feels vibration in the left-side toes, as part of the Friedreich's Ataxia Rating Scale (FARS | Time felt for toes | Numeric Values |
Educate patient regarding the sensation. Tested with 128 cps tuning fork set to near full vibration; eyes closed; test over index finger and great toe. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Supplemental | 3.00 | 2013-07-15 16:08:48.687 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Free-Form Entry |
second | |||||||||
| C11762 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination finger taps right score | FARSNeuExULCFingerTapsRtScore | The score for the right hand in the finger taps test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | The score for the right hand in the finger taps test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Finger Taps | 0;1;2;3;4 | Normal;Mild (misses 1-3 times);Moderate (misses 4-9 times);Severe (misses 10-15 times);Cannot perform the task. | Numeric Values |
Index-fingertip to thumb-crease; 15 reps as fast as possible; practice 15 reps once before rating; if time > 6 sec, add 1 to rating. Use stopwatch: |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11805 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam gait score | FARSNeuroExmUprtStabltyGaitScr | Score for the gait test in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for the gait test in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Gait | 0;1;2;3;4;5 | 0 - Normal;1 - Mild ataxia/veering/difficulty in turning, no cane/other support needed to be safe;2 - Walks with definite ataxia, may need intermittent support or examiner needs to walk with patient for safety's sake;3 - Moderate ataxia/veering/difficulty in turning, walking requires cane/holding onto examiner with one hand to be safe;4 - Severe ataxia/veering, walker or both hands of examiner needed;5 - Cannot walk even with assistance (wheelchair bound) | Numeric Values |
Tandem walk and gait are performed in a hallway. Preferably no carpet but at least serial examinations should be on the same surface. For gait place markers 25 feet apart. Patient walks the distance, turns around and comes back and the activitiy is timed. Serial examinations should be done with the same device as in the first examination. Use stopwatch; walk 8 m/25 ft at normal pace, turn around using single step pivot and return to start; performed in hallway with no furniture within reach (1 m/3 ft) and no loose carpet. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11741 | Friedreich's Ataxia Rating Scale (FARS) - daily activities cutting handling utensils score | FARSDalyActsCutUtensilScore | Cutting-food-and-handling-utensils score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS) | Cutting-food-and-handling-utensils score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS | Cutting Food and Handling Utensils | 0;0.5;1;1.5;2;2.5;3;3.5;4 | 0 - Normal;;1 - Somewhat slow and clumsy, but no help needed;;2 - Clumsy and slow but can cut most foods with some help needed, or needs assistance when in a hurry;;3 - Food must be cut by someone, but can still feed self slowly;;4 - Needs to be fed | Numeric Values |
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11773 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral nerve system muscle atrophy left score | FARSPNSNeuExMuscAtrphLfScore | Score for left-side muscle atrophy in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for left-side muscle atrophy in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Muscle Atrophy | 0;1;2 | 0 - None;1 - Present - mild/moderate;2 - Severe/total wasting | Numeric Values |
Score most severe atrophy in either upper or lower limb. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11816 | Friedreich's Ataxia Rating Scale (FARS) - instrumental testing 9 hole peg test left mean duration value | FARSInstrTest9HPTLftMeanDurVal | Mean duration in seconds for left-hand trials 1 and 2 of the 9-hole peg test in the instrumental testing section, as part of the Friedreich's Ataxia Rating Scale (FARS) | Mean duration in seconds for left-hand trials 1 and 2 of the 9-hole peg test in the instrumental testing section, as part of the Friedreich's Ataxia Rating Scale (FARS | AVG | Numeric Values |
Refer to instructions on form. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Free-Form Entry |
second | |||||||||
| C11752 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam bulbar spontaneous speech score | FARSNeuroBulbrSpontSpeechScore | The score for understandability of spontaneous speech in the bulbar portion of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | The score for understandability of spontaneous speech in the bulbar portion of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Spontaneous Speech | 0;0.5;1;1.5;2;2.5;3 | 0 - Normal;;1 - Mild (all or most words understandable);;2 - Moderate (most words not understandable);;3 - Severe (no or almost no useful speech) | Numeric Values |
Rate each item on the basis of the patient status during examination. To the extent possible, sequential patient examinations should be carried out at the same time of the day. If the patient is taking any medication, the examination should be carried out prior to dosing, or at a fixed time following the dosing based on the maximum expected therapeutic response. Increments of 0.5 may be used if examiner feels an item falls between 2 defined severities. Ask the patient to read or repeat the sentences "The President lives in the White House" or "The traffic is heavy today". |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11784 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability AFO use indicator | FARSNeuExUprtStabltyAFOUseInd | Indicator whether participant/subject is using an AFO for standing and walking assessments for Part 3: Neurological Examination E. Upright Stability, as part of the Friedreich's Ataxia Rating Scale (FARS) | Indicator whether participant/subject is using an AFO for standing and walking assessments for Part 3: Neurological Examination E. Upright Stability, as part of the Friedreich's Ataxia Rating Scale (FARS | Indicate if AFOs are used | No;Yes | No;Yes | Alphanumeric |
Record below if AFOs used. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11795 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability tandem stance trial 2 duration | FARSNEUpStbltyTaStanceTr2Dur | Duration in seconds of tandem stance trial 2 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Duration in seconds of tandem stance trial 2 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Trial 2 | 0;1;2;3;4 | 0 - 1 minute or longer;1 - <1 minute, >45 sec;2 - <45 sec, >30 sec;3 - <30 sec, >15 sec;4 - <15 sec or needs hands held by assistant/device | Numeric Values |
If a patient can stand in a particular position for 1 minute or longer in trial 1, trials 2 and 3 are abandoned. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
second | |||||||
| C17534 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral nerve system vibratory sense toe right duration | FARSPNSNeuExVibSenToeRtDur | Delay in seconds before participant/subject feels vibration in the right-side toes, as part of the Friedreich's Ataxia Rating Scale (FARS) | Delay in seconds before participant/subject feels vibration in the right-side toes, as part of the Friedreich's Ataxia Rating Scale (FARS | Time felt for toes | Numeric Values |
Educate patient regarding the sensation. Tested with 128 cps tuning fork set to near full vibration; eyes closed; test over index finger and great toe. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Supplemental | 3.00 | 2013-07-15 16:08:48.687 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Free-Form Entry |
second | |||||||||
| C11763 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination finger taps left score | FARSNeuExULCFingerTapsLftScore | The score for the left hand in the finger taps test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | The score for the left hand in the finger taps test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Finger Taps | 0;1;2;3;4 | Normal;Mild (misses 1-3 times);Moderate (misses 4-9 times);Severe (misses 10-15 times);Cannot perform the task. | Numeric Values |
Index-fingertip to thumb-crease; 15 reps as fast as possible; practice 15 reps once before rating; if time > 6 sec, add 1 to rating. Use stopwatch: |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11806 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability total value | FARSNeuroExUprtStabltyTotlVal | The sum of the scores recorded for Part 3: Neurological Examination E. Upright Stability, as part of the Friedreich's Ataxia Rating Scale (FARS) | The sum of the scores recorded for Part 3: Neurological Examination E. Upright Stability, as part of the Friedreich's Ataxia Rating Scale (FARS | Total Upright Stability Score | 0;1;2;3;4;5;6;7;8;9;10;11;12;13;14;15;16;17;18;19;20;21;22;23;24;25;26;27;28 | 0;1;2;3;4;5;6;7;8;9;10;11;12;13;14;15;16;17;18;19;20;21;22;23;24;25;26;27;28 | Numeric Values |
Enter numeric value for score of 0-28. Refer to instructions on form. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11742 | Friedreich's Ataxia Rating Scale (FARS) - daily activities dressing score | FARSDailyActivsDressingScore | Dressing score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS) | Dressing score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS | Dressing | 0;0.5;1;1.5;2;2.5;3;3.5;4 | 0 - Normal;;1 - Somewhat slow, but no help needed;;2 - Occasional assistance with buttoning, getting arms in sleeves, etc., or has to modify activity in some way (e.g., having to sit to get dressed, use velcro for shoes, stop wearing ties, etc.);;3 - Considerable help required, but can do some things alone;;4 - Helpless | Numeric Values |
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11774 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral nerve system muscle weakness right score | FARSPNSNeuExMuscWknsRtScore | Score for right-side muscle weakness in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for right-side muscle weakness in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Muscle Weakness | 0;1;2;3;4;5 | 0 - Normal (5/5);1 - Mild (movement against resistance but not full power 4/5);2 - Moderate (movement against gravity but not with added resistance 3/5);3 - Severe (movement of joint but not against gravity 2/5);4 - Near paralysis (muscular activity without movement 1/5);5 - Total paralysis (0/5) | Numeric Values |
Test deltoids, interossei, iliopsoas and tibialis anterior. Score most severe weakness in either upper or lower limb. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C17523 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral deep tendon reflex ankle jerk left score | FARSPNSNeuExDTenRAnkJLftScore | Score for left-side ankle jerk in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for left-side ankle jerk in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | AJ | 0;1;2;3;4 | 0 - absent;1 - hyporeflexia;2 - normal;3 - hyperreflexia;4 - pathologic hyperreflexia | Numeric Values | Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Supplemental | 3.00 | 2013-07-15 16:08:48.687 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11753 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam bulbar total value | FARSNeuroBulbrTotalVal | The sum of the scores recorded for Part 3: Neurological Examination A. Bulbar, as part of the Friedreich's Ataxia Rating Scale (FARS) | The sum of the scores recorded for Part 3: Neurological Examination A. Bulbar, as part of the Friedreich's Ataxia Rating Scale (FARS | Total Bulbar Score | 0;0.5;1;1.5;2;2.5;3;3.5;4;4.5;5;5.5;6;6.5;7;7.5;8;8.5;9;9.5;10;10.5;11 | 0;0.5;1;1.5;2;2.5;3;3.5;4;4.5;5;5.5;6;6.5;7;7.5;8;8.5;9;9.5;10;10.5;11 | Numeric Values |
Enter number value of 0-11. Refer to instructions on form. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11785 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability sitting posture score | FARSNeuExUprtStbltySitPostrScr | Score for sitting posture in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for sitting posture in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Sitting Posture | 0;1;2;3;4 | 0 - Normal;1 - Mild oscillations of head/trunk without touching chair back or side;2 - Moderate oscillations of head/trunk, needs contact with chair back or side for stability;3 - Severe oscillations of head/trunk, needs contact with chair back or side for stability;4 - Support on all 4 sides for stability | Numeric Values |
For sitting posture patient can sit in a chair or examination table. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11796 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability tandem stance trial 3 duration | FARSNEUpStTndmStTr3Dur | Duration in seconds of tandem stance trial 3 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Duration in seconds of tandem stance trial 3 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Trial 3 | 0;1;2;3;4 | 0 - 1 minute or longer;1 - <1 minute, >45 sec;2 - <45 sec, >30 sec;3 - <30 sec, >15 sec;4 - <15 sec or needs hands held by assistant/device | Numeric Values |
If a patient can stand in a particular position for 1 minute or longer in trial 1, trials 2 and 3 are abandoned. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
second | |||||||
| C11764 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination total value | FARSNeuExULCTotalVal | The sum of the scores recorded for Part 3: Neurological Examination B. Upper Limb Coordination, as part of the Friedreich's Ataxia Rating Scale (FARS) | The sum of the scores recorded for Part 3: Neurological Examination B. Upper Limb Coordination, as part of the Friedreich's Ataxia Rating Scale (FARS | Total Upper Limb Coordination Score | 0;1;2;3;4;5;6;7;8;9;10;11;12;13;14;15;16;17;18 | 0;1;2;3;4;5;6;7;8;9;10;11;12;13;14;15;16;17;18 | Numeric Values |
Enter numeric value of 0-36. Refer to instructions on form. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11807 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam total value | FARSNeuroExamTotalVal | The sum of the scores recorded for Part 3: Neurological Examination, as part of the Friedreich's Ataxia Rating Scale (FARS) | The sum of the scores recorded for Part 3: Neurological Examination, as part of the Friedreich's Ataxia Rating Scale (FARS | Total Neurologic Examination Score | 0;0.5;1;1.5;2;2.5;3;3.5;4;4.5;5;5.5;6;6.5;7;7.5;8;8.5;9;9.5;10;10.5;11;11.5;12;12.5;13;13.5;14;14.5;15;15.5;16;16.5;17;17.5;18;18.5;19;19.5;20;20.5;21;21.5;22;22.5;23;23.5;24;24.5;25;25.5;26;26.5;27;27.5;28;28.5;29;29.5;30;30.5;31;31.5;32;32.5;33;33.5;34;34.5;35;35.5;36;36.5;37;37.5;38;38.5;39;39.5;40;40.5;41;41.5;42;42.5;43;43.5;44;44.5;45;45.5;46;46.5;47;47.5;48;48.5;49;49.5;50;50.5;51;51.5;52;52.5;53;53.5;54;54.5;55;55.5;56;56.5;57;57.5;58;58.5;59;59.5;60;60.5;61;61.5;62;62.5;63;63.5;64;64.5;65;65.5;66;66.5;67;67.5;68;68.5;69;69.5;70;70.5;71;71.5;72;72.5;73;73.5;74;74.5;75;75.5;76;76.5;77;77.5;78;78.5;79;79.5;80;80.5;81;81.5;82;82.5;83;83.5;84;84.5;85;85.5;86;86.5;87;87.5;88;88.5;89;89.5;90;90.5;91;91.5;92;92.5;93;93.5;94;94.5;95;95.5;96;96.5;97;97.5;98;98.5;99;99.5;100;100.5;101;101.5;102;102.5;103;103.5;104;104.5;105;105.5;106;106.5;107;107.5;108;108.5;109;109.5;110;110.5;111;111.5;112;112.5;113;113.5;114;114.5;115;115.5;116;116.5;117 | 0;0.5;1;1.5;2;2.5;3;3.5;4;4.5;5;5.5;6;6.5;7;7.5;8;8.5;9;9.5;10;10.5;11;11.5;12;12.5;13;13.5;14;14.5;15;15.5;16;16.5;17;17.5;18;18.5;19;19.5;20;20.5;21;21.5;22;22.5;23;23.5;24;24.5;25;25.5;26;26.5;27;27.5;28;28.5;29;29.5;30;30.5;31;31.5;32;32.5;33;33.5;34;34.5;35;35.5;36;36.5;37;37.5;38;38.5;39;39.5;40;40.5;41;41.5;42;42.5;43;43.5;44;44.5;45;45.5;46;46.5;47;47.5;48;48.5;49;49.5;50;50.5;51;51.5;52;52.5;53;53.5;54;54.5;55;55.5;56;56.5;57;57.5;58;58.5;59;59.5;60;60.5;61;61.5;62;62.5;63;63.5;64;64.5;65;65.5;66;66.5;67;67.5;68;68.5;69;69.5;70;70.5;71;71.5;72;72.5;73;73.5;74;74.5;75;75.5;76;76.5;77;77.5;78;78.5;79;79.5;80;80.5;81;81.5;82;82.5;83;83.5;84;84.5;85;85.5;86;86.5;87;87.5;88;88.5;89;89.5;90;90.5;91;91.5;92;92.5;93;93.5;94;94.5;95;95.5;96;96.5;97;97.5;98;98.5;99;99.5;100;100.5;101;101.5;102;102.5;103;103.5;104;104.5;105;105.5;106;106.5;107;107.5;108;108.5;109;109.5;110;110.5;111;111.5;112;112.5;113;113.5;114;114.5;115;115.5;116;116.5;117 | Numeric Values |
Enter numeric value for score of 0-117. Refer to instructions on form. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11743 | Friedreich's Ataxia Rating Scale (FARS) - daily activities personal hygiene score | FARSDailyActivsPrsnlHygnScore | Personal hygiene score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS) | Personal hygiene score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS | Personal Hygiene | 0;0.5;1;1.5;2;2.5;3;3.5;4 | 0 - Normal;;1 - Somewhat slow, but no help needed;;2 - Very slow hygienic care or has need for devices such as special grab bars, tub bench, shower chair, etc.;;3 - Requires personal help with washing, brushing teeth, combing hair or using toilet;;4 - Fully dependent | Numeric Values |
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11775 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral nerve system muscle weakness left score | FARSPNSNeuExMuscWknsLftScore | Score for left-side muscle weakness in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for left-side muscle weakness in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Muscle Weakness | 0;1;2;3;4;5 | 0 - Normal (5/5);1 - Mild (movement against resistance but not full power 4/5);2 - Moderate (movement against gravity but not with added resistance 3/5);3 - Severe (movement of joint but not against gravity 2/5);4 - Near paralysis (muscular activity without movement 1/5);5 - Total paralysis (0/5) | Numeric Values |
Test deltoids, interossei, iliopsoas and tibialis anterior. Score most severe weakness in either upper or lower limb. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C17524 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral deep tendon reflex ankle jerk right score | FARSPNSNeuExDTenRAnkJRtScore | Score for right-side ankle jerk in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for right-side ankle jerk in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | AJ | 0;1;2;3;4 | 0 - absent;1 - hyporeflexia;2 - normal;3 - hyperreflexia;4 - pathologic hyperreflexia | Numeric Values | Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Supplemental | 3.00 | 2013-07-15 16:08:48.687 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11754 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination finger-finger test right score | FARSNeuExULCFingrFingrRtScore | The score for the right finger in the finger-to-finger test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | The score for the right finger in the finger-to-finger test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Finger to Finger Test | 0;1;2;3 | 0 - Normal;1 - Mild oscillations of finger (< 2 cm);2 - Moderate oscillations of finger (2-6 cm);3 - Severe oscillations of finger (> 6 cm) | Numeric Values |
The index fingers are placed in front of each other with flexion at the elbow about 25 cm from the sternum. Observe for 10 seconds. Score amplitude of oscillations: |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11786 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability stance feet apart trial 1 duration | FARSNEUprStbStncFtAprtTry1Dur | Duration in seconds of feet-apart stance trial 1 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Duration in seconds of feet-apart stance trial 1 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Trial 1 | 0;1;2;3;4 | 0 - 1 minute or longer;1 - <1 minute, >45 sec;2 - <45 sec, >30 sec;3 - <30 sec, >15 sec;4 - <15 sec or needs hands held by assistant/device | Numeric Values |
Stance assessment begins with feet 20 cm apart. Place marker tapes in the exam room 20 cm apart and the insides of the feet are lined up against these. Subsequent stance tests get more difficult. Stance and gait tests may be done barefoot if patient does not have appropriate footwear, however, it should be done the same way for serial measurement. Inside of feet 20 cm apart marked on floor. Use stopwatch; 3 attempts; time in seconds. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
second | |||||||
| C11797 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability tandem stance mean duration score | FARSNEUprtStbltyStanceTndmScr | Score for mean duration of tandem stance trials 1-3 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for mean duration of tandem stance trials 1-3 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Avg | 0;1;2;3;4 | 0 - 1 minute or longer;1 - <1 minute, >45 sec;2 - <45 sec, >30 sec;3 - <30 sec, >15 sec;4 - <15 sec or needs hands held by assistant/device | Numeric Values |
If a patient can stand in a particular position for 1 minute or longer in trial 1, trials 2 and 3 are abandoned. Otherwise each of 3 trials is timed and then averaged. Grading scores are then given as noted. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11765 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam lower limb coordination heel shin slide test position indicator | FARSNeuExLLCHeelShinSlTePosInd | Indicator of the participant/subject's position while performing heel-along-shin slide test, as part of the Friedreich's Ataxia Rating Scale (FARS) | Indicator of the participant/subject's position while performing heel-along-shin slide test, as part of the Friedreich's Ataxia Rating Scale (FARS | Supine|Seated | Supine;Seated | Supine;Seated | Alphanumeric |
May be seated with contralateral leg extended or supine but perform same way each time. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11808 | Friedreich's Ataxia Rating Scale (FARS) - instrumental testing 10 second PATA trial 1 count | FARSInstrTest10SecPATATry1Ct | Count of times participant/subject is able to repeat word "pata" in 10-sec period for trial 1 of the PATA Rate test of the instrumental testing section, as part of the Friedreich's Ataxia Rating Scale (FARS) | Count of times participant/subject is able to repeat word "pata" in 10-sec period for trial 1 of the PATA Rate test of the instrumental testing section, as part of the Friedreich's Ataxia Rating Scale (FARS | Trial 1 | Numeric Values |
Use a tape recorder that can play at slow and fast speeds (1.2 & 2.4 cm/sec). Record at normal (2.4) speed. Use a digital stopwatch. Patient seated comfortably and instructed to repeat the syllable "pata" as quickly and distinctly as possible for 10 seconds until told to stop. Start recorder and record patient's name and date. Preset stopwatch for 10 seconds. Say "go" and as soon as patient starts speaking, start timer. Say "stop" when timer beeps at end of 10 seconds. Count # of "patas" for each 10 seconds, using playback at slower speed. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Free-Form Entry |
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| C11744 | Friedreich's Ataxia Rating Scale (FARS) - daily activities falling score | FARSDailyActivsFallingScore | Falling score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS) | Falling score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS | Falling | 0;0.5;1;1.5;2;2.5;3;3.5;4 | 0 - Normal;;1 - Rare falling (< once a month);;2 - Occasional falls (once a week to once a month);;3 - Falls multiple times a week or requires device to prevent falls;;4 - Unable to stand or walk | Numeric Values |
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores. Assistive device = score 3. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11776 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral nerve system vibratory sense right score | FARSPNSNeuExVibratSenRtScore | Score for right-side vibratory sense in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for right-side vibratory sense in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Right | 0;1;2 | 0 - Normal;1 - Impaired at toes;2 - Impaired at toes or fingers | Numeric Values |
Abnormal |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C17525 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam peripheral deep tendon reflex biceps jerk left score | FARSPNSNeuExDTenRefBicJLftScr | Score for left-side biceps jerk in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Score for left-side biceps jerk in the peripheral nervous system section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | BJ | 0;1;2;3;4 | 0 - absent;1 - hyporeflexia;2 - normal;3 - hyperreflexia;4 - pathologic hyperreflexia | Numeric Values | Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Supplemental | 3.00 | 2013-07-15 16:08:48.687 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11755 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination finger-finger test left score | FARSNeuExULCFingrFingrLftScore | The score for the left finger in the finger-to-finger test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | The score for the left finger in the finger-to-finger test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Finger to Finger Test | 0;1;2;3 | 0 - Normal;1 - Mild oscillations of finger (< 2 cm);2 - Moderate oscillations of finger (2-6 cm);3 - Severe oscillations of finger (> 6 cm) | Numeric Values |
The index fingers are placed in front of each other with flexion at the elbow about 25 cm from the sternum. Observe for 10 seconds. Score amplitude of oscillations |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
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| C11787 | Friedreich's Ataxia Rating Scale (FARS) - neurological exam upright stability stance feet apart trial 2 duration | FARSNEUprStbStncFtAprtTry2Dur | Duration in seconds of feet-apart stance trial 2 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS) | Duration in seconds of feet-apart stance trial 2 in the upright stability section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS | Trial 2 | 0;1;2;3;4 | 0 - 1 minute or longer;1 - <1 minute, >45 sec;2 - <45 sec, >30 sec;3 - <30 sec, >15 sec;4 - <15 sec or needs hands held by assistant/device | Numeric Values |
If a patient can stand in a particular position for 1 minute or longer in trial 1, trials 2 and 3 are abandoned. |
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41. | Adult;Pediatric | Core | 3.00 | 2013-07-11 15:03:49.2 | Friedreich's Ataxia Rating Scale (FARS) | Ataxia and Performance Measures | Outcomes and End Points |
Single Pre-Defined Value Selected |
second |
