CDE Detailed Report

Disease: Mitochondrial Disease
Subdomain Name: Audiology
CRF: Hearing Loss in Mitochondrial Disease

Displaying 1 - 50 of 60
CDE ID CDE Name Variable Name Definition Short Description Question Text Permissible Values Description Data Type Disease Specific Instructions Disease Specific Reference Population Classification (e.g., Core) Version Number Version Date CRF Name (CRF Module / Guidance) Subdomain Name Domain Name Size Input Restrictions Min Value Max Value Measurement Type External Id Loinc External Id Snomed External Id caDSR External Id CDISC
C59823 Auditory brainstem response test perform status ABRPerfStat Status of whether auditory brainstem response (ABR) testing was performed Status of whether auditory brainstem response (ABR) testing was performed ABR/Auditory Evoked Potential Done;Not done Done;Not done Alphanumeric

Testing is used as an objective site of lesion measurement: to assess neural response integrity. Not used for determining thresholds in adults unless unable to do behavioral tests. Bone conduction is not needed in adults.

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:21.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59791 Tympanometry stimulus tone frequency type TympanometryStimToneFreqTyp Type of frequency of the stimulus tone used in tympanometry Type of frequency of the stimulus tone used in tympanometry Probe Tone 1000 Hz;226 Hz 1000 Hz;226 Hz Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:56.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Multiple Pre-Defined Values Selected

C59834 Electrocochleography perform status ElctrcchlgrphyPerfStat Status of whether electrocochleography was performed Status of whether electrocochleography was performed Electrocochleography Done;Not done Done;Not done Alphanumeric

No instructions available

No references available Adult;Pediatric Exploratory 1.00 2024-02-29 15:43:29.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59802 Audiometry threshold pure tone assessment status AudiometryThrshldPrTnAssmtStat Status indicating that pure tone audiometric thresholds were not assessed Status indicating that pure tone audiometric thresholds were not assessed Pure Tone Audiometric Thresholds Did not assess, explain Did not assess, explain Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:04.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59813 Audiometry speech recognition threshold measurement AudiometrySRTMeasr Measurement of the participant's speech recognition threshold obtained by speech audiometry Measurement of the participant's speech recognition threshold obtained by speech audiometry Speech Threshold (dB HL): SRT/SAT Numeric values

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:13.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

decibel
C59781 Otoscopy pre-auricular region abnormal type other text OtoscopyParclrRegnAbnrmlTypOTH The free-text field related to 'Otoscopy pre-auricular region abnormal type', specifying other text. Type of abnormal otoscopy finding for the pre-auricular region The free-text field related to 'Otoscopy pre-auricular region abnormal type', specifying other text. Type of abnormal otoscopy finding for the pre-auricular region Other, specify Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:48.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 4000

Free-Form Entry

C59824 Auditory brainstem response stimulus conduction type ABRStimulusConductionTyp Type of stimulus conduction used for auditory brainstem response (ABR) testing Type of stimulus conduction used for auditory brainstem response (ABR) testing ABR/Auditory Evoked Potential Bone conduction;Air conduction Bone conduction;Air conduction Alphanumeric

Testing is used as an objective site of lesion measurement: to assess neural response integrity. Not used for determining thresholds in adults unless unable to do behavioral tests. Bone conduction is not needed in adults.

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:21.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59792 Tympanometry ear canal volume measurement TympanometryEarCanalVolumMeasr Measurement of ear canal volume obtained by tympanometry Measurement of ear canal volume obtained by tympanometry Ear Canal Volume (cc) Numeric values

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:57.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

cubic centimeter
C59803 Audiometry threshold pure tone alternative stimulus text AudiomtryThrshldPrTnAltStimTxt Free-text field describing the alternative stimuli used in pure tone audiometric threshold testing Free-text field describing the alternative stimuli used in pure tone audiometric threshold testing Alternative stimuli Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:05.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 255

Free-Form Entry

C59835 Electrocochleography result status ElctrcchlgrphyResltStat Status of the result of the electrocochleography test performed Status of the result of the electrocochleography test performed Result Abnormal;Normal Abnormal;Normal Alphanumeric

No instructions available

No references available Adult;Pediatric Exploratory 1.00 2024-02-29 15:43:30.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59814 Audiometry speech awareness threshold measurement AudiometrySATMeasr Measurement of the participant's speech awareness threshold obtained by speech audiometry Measurement of the participant's speech awareness threshold obtained by speech audiometry Speech Threshold (dB HL): SRT/SAT Numeric values

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:14.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

decibel
C59782 Otoscopy pinna abnormal type OtoscopyPinnaAbnrmlTyp Type of abnormal otoscopy finding for the pinna Type of abnormal otoscopy finding for the pinna Abnormal, explain Location;Microtia;Shape;Size;Other, specify Location;Microtia;Shape;Size;Other, specify Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:49.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Multiple Pre-Defined Values Selected

C59825 Auditory brainstem response stimulus type ABRStimulusTyp Type of stimulus used for auditory brainstem response (ABR) testing Type of stimulus used for auditory brainstem response (ABR) testing Stimulus Tone;click Tone;click Alphanumeric

Testing is used as an objective site of lesion measurement: to assess neural response integrity. Not used for determining thresholds in adults unless unable to do behavioral tests. Bone conduction is not needed in adults.

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:22.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59793 Tympanometry compensated amplitude measurement TympanometryCompenstdAmpMeasur Measurement of compensated amplitude obtained by tympanometry Measurement of compensated amplitude obtained by tympanometry Compensated Amplitude Numeric values

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:57.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

millimhos
C59804 Audiometry test location AudiometryTestLoc Location of audiometry test Location of audiometry test Test location Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:06.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 255

Free-Form Entry

C59836 Electrocochleography abnormal result text ElctrcchlgrphyAbnrmlResltTxt Free-text field describing the abnormal result of the electrocochleography test Free-text field describing the abnormal result of the electrocochleography test Abnormal, explain Alphanumeric

No instructions available

No references available Adult;Pediatric Exploratory 1.00 2024-02-29 15:43:31.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 255

Free-Form Entry

C59815 Audiometry word recognition score AudiometryWordRecognitionScore Score for word recognition obtained by speech audiometry Score for word recognition obtained by speech audiometry Word Recognition Numeric values

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:14.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

C59783 Otoscopy pinna abnormal type other text OtoscopyPinnaAbnrmlTypOTH The free-text field related to 'Otoscopy pinna abnormal type', specifying other text. Type of abnormal otoscopy finding for the pinna The free-text field related to 'Otoscopy pinna abnormal type', specifying other text. Type of abnormal otoscopy finding for the pinna Other, specify Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:50.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 4000

Free-Form Entry

C59826 Auditory brainstem response stimulus level measurement ABRStimulusLvlMeasr Measurement of the stimulus used for auditory brainstem response (ABR) testing Measurement of the stimulus used for auditory brainstem response (ABR) testing Stimulus Level Numeric values

Testing is used as an objective site of lesion measurement: to assess neural response integrity. Not used for determining thresholds in adults unless unable to do behavioral tests. Bone conduction is not needed in adults.

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:23.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

decibel
C59794 Tympanometry peak pressure measurement TympanometryPeakPressureMeasur Measurement of peak pressure obtained by tympanometry Measurement of peak pressure obtained by tympanometry Peak (daPa) Numeric values

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:58.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

decapascal
C59805 Audiometry transducer type AudiometryTransducerTyp Type of transducer used for audiometry Type of transducer used for audiometry Transducer used Headphones/insert;Bone vibrator;Non-ear specific/speakers Headphones/insert;Bone vibrator;Non-ear specific/speakers Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:07.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59816 Audiometry speech test score AudiometrySpeechTestScore Score for the speech audiometry test Score for the speech audiometry test Score Numeric values

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:15.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

C59784 Otoscopy external auditory canal abnormal type OtoscopyExtAdtyCnlAbnrmlTyp Type of abnormal otoscopy finding for the external auditory canal Type of abnormal otoscopy finding for the external auditory canal Abnormal, explain Atresia;Cerumen impaction;Edema;Erythema;Erythema annulare centrifugum (EAC);Granulation tissue;Stenosis;Other, specify Atresia;Cerumen impaction;Edema;Erythema;Erythema annulare centrifugum (EAC);Granulation tissue;Stenosis;Other, specify Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:50.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Multiple Pre-Defined Values Selected

C59827 Auditory brainstem response threshold measurement ABRThresholdMeasr Measurement of the hearing threshold obtained by auditory brainstem response (ABR) testing Measurement of the hearing threshold obtained by auditory brainstem response (ABR) testing Threshold Numeric values

Testing is used as an objective site of lesion measurement: to assess neural response integrity. Not used for determining thresholds in adults unless unable to do behavioral tests. Bone conduction is not needed in adults.

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:24.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

decibel
C59795 Tympanometry gradient measurement TympanometryGradientMeasur Measurement of the gradient with an ear canal volume correction of 200 decapascals (daPa) obtained by tympanometry Measurement of the gradient with an ear canal volume correction of 200 decapascals (daPa) obtained by tympanometry Gradient (re: +200) Numeric values

No instructions available

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:42:59.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

decapascal
C59806 Audiometry threshold pure tone air conduction stimulus frequency type AudiometryThrshPrTnArCnStFrTyp Type of frequency of the stimulus presented for pure tone audiometric threshold air conduction testing Type of frequency of the stimulus presented for pure tone audiometric threshold air conduction testing Air conduction thresholds 6000 Hz;125 Hz;250 Hz;500 Hz;750 Hz;1000 Hz;1500 Hz;2000 Hz;3000 Hz;4000 Hz;8000 Hz;9000 Hz;10000 Hz;11200 Hz;12500 Hz;14000 Hz;16000 Hz;18000 Hz;20000 Hz 6000 Hz;125 Hz;250 Hz;500 Hz;750 Hz;1000 Hz;1500 Hz;2000 Hz;3000 Hz;4000 Hz;8000 Hz;9000 Hz;10000 Hz;11200 Hz;12500 Hz;14000 Hz;16000 Hz;18000 Hz;20000 Hz Alphanumeric

Core: 250 Hz;500 Hz;1000 Hz;2000 Hz;3000 Hz;4000 Hz;6000 Hz;8000 Hz
Supplemental - Highly Recommended: 125 Hz; 750 Hz; 1500 Hz
Extended high frequencies are Supplemental - Highly Recommended for the adult population and Exploratory for the pediatric population

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:07.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Multiple Pre-Defined Values Selected

C59817 Audiometry speech hearing level measurement AudiometrySpeechHrLvMeasr Measurement of hearing level obtained by speech audiometry Measurement of hearing level obtained by speech audiometry Level (dB HL) Indicate Numeric values

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:16.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

decibel
C59785 Otoscopy external auditory canal abnormal type other text OtoscopyExtAdtyCnlAbnrmlTypOTH The free-text field related to 'external auditory canal abnormal type', specifying other text. Type of abnormal otoscopy finding for the external auditory canal The free-text field related to 'external auditory canal abnormal type', specifying other text. Type of abnormal otoscopy finding for the external auditory canal Other, specify Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:51.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 4000

Free-Form Entry

C59828 Auditory brainstem response latency measurement ABRLatencyMeasr Measurement of the wave latency obtained by auditory brainstem response (ABR) testing Measurement of the wave latency obtained by auditory brainstem response (ABR) testing Latency Numeric values

Testing is used as an objective site of lesion measurement: to assess neural response integrity. Not used for determining thresholds in adults unless unable to do behavioral tests. Bone conduction is not needed in adults.

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:25.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

0 millisecond
C59796 Tympanometry middle ear resonance estimate measurement TympanometryMdEarRsncEstMeasur Measurement of the estimated middle ear resonance obtained by tympanometry Measurement of the estimated middle ear resonance obtained by tympanometry Est. Middle Ear Resonance Numeric values

No instructions available

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:00.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

hertz
C59807 Audiometry threshold pure tone hearing level measurement AudiometryThrshldPrTnHrLvMeasr Measurement of hearing level threshold obtained by pure tone audiometry Measurement of hearing level threshold obtained by pure tone audiometry dB HL Numeric values

Record threshold
Mild: 20-34 dB
Moderate: 35-49 dB
Moderately Severe: 50-64 dB
Severe: 65-79 dB
Profound: 80-94 dB
Complete: 95+ dB

World report on hearing. Geneva: World Health Organization; 2021. License: CC<br />BY-NC-SA 3.0 IGO. Adult;Pediatric Core 1.00 2024-02-29 15:43:08.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

decibel
C59818 Otoacoustic emission test perform status OAETestPerfStat Status of whether otoacoustic emissions testing was performed Status of whether otoacoustic emissions testing was performed OAEs Done;Not done Done;Not done Alphanumeric

Testing is used as an objective site of lesion measurement: functional integrity of the cochlear outer hair cell subsystem. Present OAEs are defined as 6 dB SNR.

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:17.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59786 Otoscopy tympanic membrane abnormal type OtoscopyTympncMmbnAbnrmlTyp Type of abnormal otoscopy finding for the tympanic membrane Type of abnormal otoscopy finding for the tympanic membrane Abnormal, explain Erythematous;Granulation tissue;Immobile;Indwelling tympanostomy tube;Opaque;Otorrhea;Perforation;Retraction;Other, specify Erythematous;Granulation tissue;Immobile;Indwelling tympanostomy tube;Opaque;Otorrhea;Perforation;Retraction;Other, specify Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:52.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Multiple Pre-Defined Values Selected

C59829 Auditory steady state response threshold measurement ASSRThresholdMeasr Measurement of the hearing threshold obtained by auditory steady state response (ASSR) Measurement of the hearing threshold obtained by auditory steady state response (ASSR) ASSR Numeric values

No instructions available

No references available Adult;Pediatric Exploratory 1.00 2024-02-29 15:43:25.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

0 120 decibel
C59797 Acoustic reflex test perform status AcousticReflexPerfStat Status of whether acoustic reflex testing was performed Status of whether acoustic reflex testing was performed Acoustic Reflexes Done;Not done Done;Not done Alphanumeric

No instructions available

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:01.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59808 Audiometry masking status AudiometryMaskStat Status of masking used in audiometry Status of masking used in audiometry Masking Status Unmasked;Masked Unmasked;Masked Alphanumeric

Ear specific bone conduction values are presumed to be masked. Non-specific values are presumed to be unmasked

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:09.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59819 Otoacoustic emission test type OAETestTyp Type of otoacoustic emission test performed Type of otoacoustic emission test performed OAEs TEOAEs;DPOAEs TEOAEs;DPOAEs Alphanumeric

Testing is used as an objective site of lesion measurement: functional integrity of the cochlear outer hair cell subsystem. Present OAEs are defined as 6 dB SNR.

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:17.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Multiple Pre-Defined Values Selected

C59787 Otoscopy tympanic membrane abnormal type other text OtoscopyTympncMmbnAbnrmlTypOTH The free-text field related to 'tympanic membrane abnormal type', specifying other text. Type of abnormal otoscopy finding for the tympanic membrane The free-text field related to 'tympanic membrane abnormal type', specifying other text. Type of abnormal otoscopy finding for the tympanic membrane Other, specify Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:53.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 4000

Free-Form Entry

C59830 Auditory brainstem response wave peak latency measurement ABRWavePeakLatencyMeasr Measurement of wave peak latency obtained by auditory brain stem response (ABR) testing Measurement of wave peak latency obtained by auditory brain stem response (ABR) testing Wave Peak Latencies Numeric values

Testing is used as an objective site of lesion measurement: to assess neural response integrity. Not used for determining thresholds in adults unless unable to do behavioral tests. Bone conduction is not needed in adults.

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:26.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Free-Form Entry

0 millisecond
C59798 Acoustic reflex stimulus tone frequency type AcousticReflexStimToneFreqTyp Type of frequency of the stimulus tone used in acoustic reflex testing Type of frequency of the stimulus tone used in acoustic reflex testing Tone Activator 2000 Hz;1000 Hz;500 Hz 2000 Hz;1000 Hz;500 Hz Alphanumeric

No instructions available

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:01.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Multiple Pre-Defined Values Selected

C59809 Audiometry threshold pure tone bone conduction stimulus frequency type AudiometryThrshPrTnBnCnStFrTyp Type of frequency of the stimulus presented for pure tone audiometric threshold bone conduction testing Type of frequency of the stimulus presented for pure tone audiometric threshold bone conduction testing Bone conduction thresholds 250 Hz;500 Hz;750 Hz;1000 Hz;1500 Hz;2000 Hz;3000 Hz;4000 Hz 250 Hz;500 Hz;750 Hz;1000 Hz;1500 Hz;2000 Hz;3000 Hz;4000 Hz Alphanumeric

Core: 251 Hz;500 Hz;1000 Hz;2000 Hz;3000 Hz;4000 Hz;
Supplemental - Highly Recommended: 750 Hz; 1500 Hz
Ear specific bone conduction values are presumed to be masked. Non-specific values are presumed to be unmasked

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:10.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Multiple Pre-Defined Values Selected

C59777 Otoscopy anatomic site OtoscopyAnatSite Anatomic site of the otoscopy Anatomic site of the otoscopy Otoscopy result Tympanic membrane;External auditory canal;Pinna;Pre-auricular region Tympanic membrane;External auditory canal;Pinna;Pre-auricular region Alphanumeric

Examination informs regarding status of the external canal, tympanic membrane, middle ear

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:45.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59820 Otoacoustic emission present frequency text OAEPresentFreqTxt Free-text field listing the frequencies with present otoacoustic emissions (OAEs) Free-text field listing the frequencies with present otoacoustic emissions (OAEs) Present (frequencies) Alphanumeric

Testing is used as an objective site of lesion measurement: functional integrity of the cochlear outer hair cell subsystem. Present OAEs are defined as 6 dB SNR.

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:18.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 255

Free-Form Entry

C59788 Tympanometry assessment status TympanometryAssmtStat Status indicating that tympanometry was not assessed Status indicating that tympanometry was not assessed Tympanometry Did not assess, explain Did not assess, explain Alphanumeric

Testing informs regarding objective site of lesion measurement: functional integrity of the sound-conduction system (ear canal patency, tympanic membrane mobility, middle ear status)

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:53.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59831 Auditory brainstem response wave peak number ABRWavePeakNumber Number(s) of the wave peak(s) measured in auditory brainstem response (ABR) testing Number(s) of the wave peak(s) measured in auditory brainstem response (ABR) testing Wave Peak Latencies I;III;IV I;III;IV Numeric values

Testing is used as an objective site of lesion measurement: to assess neural response integrity. Not used for determining thresholds in adults unless unable to do behavioral tests. Bone conduction is not needed in adults.

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:27.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59799 Acoustic reflex test condition type AcousticReflexTestCondTyp Type of test condition for the acoustic reflex testing Type of test condition for the acoustic reflex testing Acoustic Reflexes Probe Right, Stimulus Left;Probe Right, Stimulus Right;Probe Left, Stimulus Right;Probe Left, Stimulus Left Probe Right, Stimulus Left;Probe Right, Stimulus Right;Probe Left, Stimulus Right;Probe Left, Stimulus Left Alphanumeric

No instructions available

No references available Adult;Pediatric Supplemental-Highly Recommended 1.00 2024-02-29 15:43:02.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59810 Audiometry speech assessment status AudiometrySpeechAssmtStat Status indicating that speech audiometry was not assessed Status indicating that speech audiometry was not assessed Speech audiometry Did not assess, explain Did not assess, explain Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:11.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59778 Otoscopy result status OtoscopyRsltStat Status of otoscopy result Status of otoscopy result Otoscopy result Abnormal, explain;Exam not done;Cannot assess, explain;Normal;Normal (translucent and mobile) Abnormal, explain;Exam not done;Cannot assess, explain;Normal;Normal (translucent and mobile) Alphanumeric

Examination informs regarding status of the external canal, tympanic membrane, middle ear

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:46.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations

Single Pre-Defined Value Selected

C59821 Otoacoustic emission absent frequency text OAEAbsentFreqTxt Free-text field listing the frequencies with absent otoacoustic emissions (OAEs) Free-text field listing the frequencies with absent otoacoustic emissions (OAEs) Absent (frequencies) Alphanumeric

Testing is used as an objective site of lesion measurement: functional integrity of the cochlear outer hair cell subsystem. Present OAEs are defined as 6 dB SNR.

No references available Adult;Pediatric Core 1.00 2024-02-29 15:43:19.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 255

Free-Form Entry

C59789 Audiometry test not perform text AudiometryTestNotPerfTxt Free-text field describing why an audiometry test was not performed Free-text field describing why an audiometry test was not performed Did not assess, explain Alphanumeric

No instructions available

No references available Adult;Pediatric Core 1.00 2024-02-29 15:42:54.0 Hearing Loss in Mitochondrial Disease Audiology Assessments and Examinations 255

Free-Form Entry

CSV